Journal of Kerman University of Medical Sciences

Renal Angiomyolipoma Associated with Renal Vein and Inferior Vena Cava Thrombosis: A Case Report

Document Type : Case Report

Authors

Reza Mohammadi 1
Ali Kamalati 1
Mohammadali Bagherinasabsarab 1
Elham Jafari 2
Fatemeh Yazdanpanah 3

1 Department of Urology, Kerman University Medical Sciences, Kerman, Iran

2 Pathology and Stem Cell Research Center, Pathology department, Kerman University of Medical Science, Kerman, Iran

3 Department of Dermatology, Kerman University of Medical Sciences, Kerman, Iran

https://doi.org/10.34172/jkmu.2023.09
Abstract
Abstract
Angiomyolipoma (AML) is the most common benign renal mesenchymal neoplasm. This is a report of a 36-year-old female patient with AML with the involvement of the inferior vena cava (IVC) who was admitted to our hospital. The patient complained of mild right flank pain. CT scan results showed a hypo-dense mass with 47 × 72 mm dimensions at the right kidney›s lower pole suggesting renal AML. In MRI with contrast, venous thrombosis was detected in the right renal vein and IVC. Right radical nephrectomy and IVC thrombectomy were successfully conducted. Renal AML was confirmed by pathological findings, and the presence of tumor thrombosis was approved in the right renal vein and IVC. Although AML is generally benign and vascular invasion is a rare finding in this condition, imaging studies (including CT scans) should always be considered to determine the extent of vascular involvement and choose an appropriate therapeutic plan, including nephrectomy and thrombectomy in case of vascular involvement. Despite its benign nature, it should be considered that AML can invade venous structures in the kidneys. Early imaging studies and therapeutic interventions are necessary for obtaining the best outcome.
 

Keywords

Keywords: Angiomyolipoma
Flank pain
Inferior vena cava thrombosis
Kidney
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Journal of Kerman University of Medical Sciences
Volume 30, Issue 1
January and February 2023
Pages 55-57

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