Journal of Kerman University of Medical Sciences

Report of a Successful Aortic Dissection Surgery in a Patient with Marfan Syndrome: Management of Cardiopulmonary Bypass

Articles in Press

Document Type : Case Report

Authors

Ahmad Amouzeshi 1
Mahmoud Ganjifard 2
Azam Rezaei 3
Mohammad Bakhtiari 4
Maryam Ghadimi 5
Yasamin Chaibakhsh 5
Maryam Bahramian 6
Mozhgan Bahramian 6
Seyyed Ebrahim Hosseini Zargaz 7

1 Department of Cardiology, School of Medicine, Cardiovascular Diseases Research Center, Birjand University of Medical Sciences, Birjand, Iran

2 Department of Anesthesiology and Critical Care, Faculty of Medicine, Birjand University of Medical Sciences, Birjand, Iran

3 Department of Internal Medicine, School of Medicine, Birjand University of Medical Sciences, Birjand, Iran

4 School of Medical Sciences, Sirjan School of Medical Sciences, Kerman, Iran

5 Cardiovascular Research Center, Rajaie Cardiovascular Institute, Tehran, Iran

6 Department of Social Medicine, School of Medicine, Birjand University of Medical Sciences, Birjand, Iran

7 Cardiovascular Diseases Research Center, Birjand University of Medical Sciences, Birjand, Iran

Abstract
Background: Aortic dissection is a rare emergency type A aortic dissection associated with Marfan syndrome is a rare emergency condition that typically occurs in young individuals. Mortality and morbidity rates in these patients are higher compared to those of other open-heart surgeries.
Case Report: We report a 31-year-old man with Marfan syndrome who presented to our center with chest pain. A CT angiography confirmed a diagnosis of type A aortic dissection. The patient underwent open-heart surgery, during which a moderate hypothermia technique, along with systemic arrest, was utilized during cardiopulmonary bypass. Following the operation, he was transferred to the intensive care unit and was ultimately discharged after seven days.
Conclusion: Although aortic dissection is a rare emergency condition, a series of protective measures during cardiopulmonary bypass (CPB), such as systemic arrest and other considerations, can prevent complications arising from prolonged bypass time and hypothermia. Furthermore, surgical techniques and cardiopulmonary bypass management both play significant roles in surgical outcomes.

Keywords

Aortic Dissection
Marfan Syndrome
Cardiopulmonary Bypass
Subjects
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Journal of Kerman University of Medical Sciences

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